Sebaceous hyperplasia is a common and benign disorder of the sebaceous gland. It commonly develops in middle aged to elderly persons, but the premature type can appear at puberty. Sebaceous hyperplasia usually presents as yellowish, scattered umbilicated papules on the forehead, nose, and cheeks. The term "sebaceous hyperplasia en plaque" means that numerous sebaceous hyperplasia papules are present in a grouped, plaque-like pattern. No reports of development of sebaceous hyperplasia with nevus sebaceus on the same distribution are available. Herein, we report a case of premature sebaceous hyperplasia en plaque with nevus sebaceus of the same distribution.