Most common anterior mediastinal mass is thymoma, lymphoma and teratoma. Sarcomas are rare connective tissue malignant neoplasm which can be affected various locations, most frequently occur in the extremities. In fact, primary mediastinal sarco-mas are extremely uncommon, less than 2% of all soft tissue sarcoma cases. The majority of primary thoracic sarcomas are originated from chest wall, pleural spaces and nerve sheath. Therefore, the primary thoracic sarcomas involved in the lung parenchyma are rarer with poor information regarding the proper management and its outcomes. Herein, we report a rare and interesting case of primary thoracic high-grade sarcoma occupying anterior mediastinum and left lower lobe of the lung of a 35-years-old man, with reviewing the previous reports and literatures.