Noncompaction of ventricle is unclassified cardiomyopathy with genetic problem and associated with other congenital cardiac anomaly. Clinical manifestation of noncompaction of ventricle is variable including LV dysfunction, chest pain, thromboembolic event, and arrhythmia. We reported noncompaction with bradyarrhythmia manifestation, especially complete atrioventricular block. Male, 59 years old patient was visited outpatient with history of syncope on July, 2011. In routine check up in Autumn 2010, EKG was normal and he didn``t have any other medical history. Initial EKG finding was complete AV block ECHO Finding : LV Ejection fraction was 25~30% with Left and Right ventricle non-compaction Permenant pacemaker was inserted for atrioventricular block Β-blocker, ACE inhibitor and Diuretics was add for LV dysfunction At dischare, he had no complaint of syncope or dyspnea. In our case, complete atrioventricular block with syncope was first manifestation of noncompaction, especially biventricular. In a near future, cardioverter will be also considered for primary prevention of ventricular arrhythmia. |