Clinical manifestations
: severe rest pain, coolness, pallor of the lower extremities and the absence of distal pulses bilaterally
Diagnosis should be established rapidly by MRI, CT
Emergency thrombectomy or revascularization is indicated
It often affects the ascending aorta and aortic arch, causing obstruction of the aorta and its major arteries
Pulseless disease
Management
Three factors that usually are considered
1) Fetal age and thus maturity
2) Labor
3) Bleeding and its severity
? Preterm + no persistent active bleeding
→ Close observation
? Near term + not bleeding
→ Scheduled cesarean delivery
※ Timing is important to maximize fetal growth but to minimize the possibility of antepartum hemorrhage.
※ Data are sparse rega
factor V Leiden와 같은 인자들에 의해서 발병하고 있다. 최근연구에서 혈장내 고농도의 VII인자가 혈전(thrombosis)을 발생시키는 것으로 보고하고으며, 가장 흔한 선천성 혈액질환으로 혈우병(hemophila A), von Willebrand's 질병이다. 각 질환의 발병율은 18-1에 나타나 있다.
응고장애는 일생의 어떤 단계에서도